Protein turnover in acid maltase deficiency before and after treatment with a high protein diet.
نویسندگان
چکیده
A patient with acid maltase deficiency was treated with a high protein diet for 7 months. Protein turnover expressed in terms of lean body mass was shown to be increased in this patient before the diet but was markedly reduced following the diet. The patient improved clinically whilst on the diet both subjectively and in terms of mobility, breathing and reduced peripheral cyanosis at rest.
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ورودعنوان ژورنال:
- Journal of neurology, neurosurgery, and psychiatry
دوره 50 5 شماره
صفحات -
تاریخ انتشار 1987